ALVEOLAR TYPE OF ADULT ORBITAL RHABDOMYOSARCOMA: A CASE REPORT.

Niemah BASRI¹, Nur Asyilla CHE JALIL^2,3, Aniza HASSAN⁴, Ahmad Hadif Zaidin SAMSUDIN^1,3.

¹Department of Radiology, ²Department of Pathology, School of Medical sciences, Universiti Sains Malaysia, Health Campus, 16150 Kubang Kerian, Kelantan, Malaysia. ³Hospital Universiti Sains Malaysia, 16150 Kubang Kerian, Kelantan, Malaysia, and ⁴Department of Pathology, Hospital Raja Perempuan Zainab II, 15586 Kota Bharu, Kelantan, Malaysia.

ABSTRACT

Rhabdomyosarcoma is a soft tissue tumour of undifferentiated mesenchymal cells that commonly occurs in the paediatric age group, particularly the embryonal subtype. Pleomorphic rhabdomyosarcoma usually occurs in an adult. On the other hand, alveolar rhabdomyosarcoma can affect all age groups. The common site of alveolar rhabdomyosarcoma is mainly the extremities. Embryonal rhabdomyosarcoma usually affects the head and neck region as well as the genitourinary tract. Only 10% of overall rhabdomyosarcoma involved the orbital region. Imaging features of rhabdomyosarcoma may not be specific; however, early suspicion based on radiological imaging may help in the patient’s management and treatment course. We report a rare case of orbital rhabdomyosarcoma, an alveolar subtype in a 54 year-old-woman. The aim of this case report is to discuss the clinicopathological features of this type of tumour in an adult.

Keywords: Alveolar rhabdomyosarcoma,  Adult, Orbital neoplasm, Chemo-radiotherapy, Radiological imaging.

Corresponding author: Ahmad Hadif Zaidin Samsudin, Department of Radiology, School of Medical Sciences, Universiti Sains Malaysia Health Campus 16150 Kota Bharu, Kelantan, Malaysia.

Email: hadif@usm.my

Brunei Int Med J.2022;18:144-148